BREAKTHROUGH OF THE YEAR

1.     It's All About Me

2.     Human Genetic Variation

 

1.       It's All About Me

Jocelyn Kaiser

Along with the flood of discoveries in human genetics, 2007 saw the birth of a new industry: personal genomics. Depending on your budget, you can either buy a rough scan of your genome or have the whole thing sequenced. The companies say the information will help customers learn about themselves and improve their health. But researchers worry that these services open up a Pandora's box of ethical issues.

At $300,000 to $1 million per genome, sequencing all 3 billion base pairs is still too costly for all but a few. Although dozens more personal genomes will probably be sequenced in the coming year, most will be done by public and private research organizations--including the institute run by genome maverick J. Craig Venter, whose personal genome was one of three completed in 2007 in the United States and China. In a lower-budget effort, Harvard's George Church this month will deliver initial DNA sequences for the protein-coding sections (1% of the genome) to the first 10 volunteers for his Personal Genome Project. Meanwhile, a new company called Knome is offering full-genome sequencing to 20 customers willing to pay $350,000.

A glimpse of one's genome is already within the reach of ordinary people, thanks to several companies. They include 23andMe, which has financing from Google and may let users link to others with shared traits; Navigenics, which will screen for about 20 medical conditions; and deCODE Genetics in Iceland, a pioneer in disease gene hunting. For $1000 to $2500, these companies will have consumers send in a saliva sample or cheek swab, then use "SNP chips" to scan their DNA for as many as 1 million markers. The companies will then match the results with the latest publications on traits, common diseases, and ancestry.

Although many customers may view this exercise as a way to learn fun facts about themselves--recreational genomics, some call it--bioethicists are wary. Most common disease markers identified so far raise risks only slightly, but they could cause needless worry. At the same time, some people may be terrified to learn they have a relatively high risk for an incurable disease such as Alzheimer's.

The rush toward personal genome sequences also sharpens long-held worries about discrimination. A bill to prevent insurers and employers from misusing genetic data is stalled in Congress. Complicating matters, your genetic information exposes your relatives' DNA, too.

The most profound implications of having one's genome analyzed may not be what it reveals now--which isn't much--but what it may show later on. Perhaps to sidestep such questions, some companies will limit which markers to disclose. Others, however, will hand customers their entire genetic identity, along with all the secrets it may hold.

Papers and articles related to personal genomics

A.L. McGuire, "The Future of Personal Genomics," Science 317, 1687 (2007)

S. Levy et al., "The Diploid Genome Sequence of an Individual Human," PLoS Biology 5, e254 (2007)

J. Cohen, "Venter's Genome Sheds New Light on Human Variation," Science 317, 1311 (2007)

E. Marshall, "Sequencers of a Famous Genome Confront Privacy Issues," Science 315, 1780 (2007)

C. Holden, "Long-Awaited Genetic Nondiscrimination Bill Headed for Easy Passage," Science 316, 676 (2007)

Interesting Websites

Knome, Inc.
Personal genomics company that offers whole-genome sequencing and analysis services for individuals.

23andMe, Inc.
Company dedicated to helping individuals understand their own genetic information using recent advances in DNA analysis technologies and web-based interactive tools.

Navigenics, Inc.
Provides customers with information about their genetic predispositions for certain diseases.

deCODE Genetics, Inc.
A biopharmaceutical company applying its discoveries in human genetics to the development of drugs and diagnostics for common diseases.

 

2.       Human Genetic Variation

Elizabeth Pennisi

The unveiling of the human genome almost 7 years ago cast the first faint light on our complete genetic makeup. Since then, each new genome sequenced and each new individual studied has illuminated our genomic landscape in ever more detail. In 2007, researchers came to appreciate the extent to which our genomes differ from person to person and the implications of this variation for deciphering the genetics of complex diseases and personal traits.

Less than a year ago, the big news was triangulating variation between us and our primate cousins to get a better handle on genetic changes along the evolutionary tree that led to humans. Now, we have moved from asking what in our DNA makes us human to striving to know what in my DNA makes me me.

Techniques that scan for hundreds of thousands of genetic differences at once are linking particular variations to particular traits and diseases in ways not possible before. Efforts to catalog and assess the effects of insertions and deletions in our DNA are showing that these changes are more common than expected and play important roles in how our genomes work--or don't work. By looking at variations in genes for hair and skin color and in the "speech" gene, we have also gained a better sense of how we are similar to and different from Neandertals.

Already, the genomes of several individuals have been sequenced, and rapid improvements in sequencing technologies are making the sequencing of "me" a real possibility. The potential to discover what contributes to red hair, freckles, pudginess, or a love of chocolate--let alone quantifying one's genetic risk for cancer, asthma, or diabetes--is both exhilarating and terrifying. It comes not only with great promise for improving health through personalized medicine and understanding our individuality but also with risks for discrimination and loss of privacy.

Turning on the flood lamps
Even with most of the 3 billion DNA bases lined up in the right order, there was still much that researchers couldn't see in the newly sequenced human genome in 2001. Early comparative studies threw conserved regulatory regions, RNA genes, and other features into relief, bringing meaning to much of our genome, including the 98% that lies outside protein-coding regions. These and other studies, including a pilot study called ENCODE, completed this year, drove home how complex the genome is.

There are an estimated 15 million places along our genomes where one base can differ from one person or population to the next. By mid-2007, more than 3 million such locations, known as single-nucleotide polymorphisms (SNPs), had been charted. Called the HapMap, this catalog has made the use of SNPs to track down genes involved in complex diseases--so-called genome-wide association studies--a reality. More than a dozen such studies were published this year.

Traditionally, geneticists have hunted down genes by tracking the inheritance of a genetic disease through large families or by searching for suspected problematic genes among patients. Genome-wide association studies go much further. They compare the distribution of SNPs--using arrays that can examine some 500,000 SNPs at a time--in hundreds or even thousands of people with and without a particular disease. By tallying which SNPs co-occur with symptoms, researchers can determine how much increased risk is associated with each SNP.

In the past, such links have been hard-won, and most have vanished on further study. This year, however, researchers linked variants of more than 50 genes to increased risk for a dozen diseases. Almost all the variants exert relatively small effects, in concert with many other genetic factors and environmental conditions, and in many cases the variant's real role has not yet been pinned down. But the sheer numbers of people studied have made even skeptics hopeful that some of these genetic risk factors will prove real and will help reveal underlying causes.

The Wellcome Trust, the U.K.'s largest biomedical charity, began to put its weight behind genome-wide association studies in 2005 and recruited 200 researchers to analyze the DNA of 17,000 people from across the United Kingdom. The results are part of an avalanche of genetic information becoming available as more and more geneticists agree to share data and as funding agencies require such exchanges. In June, the consortium published a mammoth analysis of seven diseases, including rheumatoid arthritis, bipolar disorder, and coronary artery disease. It also found several gene variants that predispose individuals to type 1 diabetes and three new genes for Crohn's disease.

Several large studies have also pinpointed type 2 diabetes genes. One French study involving nonobese diabetics found that a version of a gene for a protein that transports zinc in the pancreas increased the risk of this disease. Three simultaneous reports involving more than 32,000 participants uncovered four new diabetes-associated gene variants, bringing to 10 the number of known non-Mendelian genetic risk factors for type 2 diabetes. These finds strongly point to pancreatic beta cells as the source of this increasingly common chronic disorder.

New gene associations now exist for heart disease, breast cancer, restless leg syndrome, atrial fibrillation, glaucoma, amyotrophic lateral sclerosis, multiple sclerosis, rheumatoid arthritis, colorectal cancer, ankylosing spondylitis, and autoimmune diseases. One study even identified two genes in which particular variants can slow the onset of AIDS, demonstrating the potential of this approach for understanding why people vary in their susceptibility to infectious diseases.

Genomic hiccups
Genomes can differ in many other ways. Bits of DNA ranging from a few to many thousands, even millions, of bases can get lost, added, or turned around in an individual's genome. Such revisions can change the number of copies of a gene or piece of regulatory DNA or jam two genes together, changing the genes'products or shutting them down. This year marked a tipping point, as researchers became aware that these changes, which can alter a genome in just a few generations, affect more bases than SNPs.

In one study, geneticists discovered 3600 so-called copy number variants among 95 individuals studied. Quite a few overlapped genes, including some implicated in our individuality--blood type, smell, hearing, taste, and metabolism, for example. Individual genomes differed in size by as many as 9 million bases. This fall, another group performed an extensive analysis using a technique, called paired-end mapping, that can quickly uncover even smaller structural variations.

These differences matter. One survey concluded that in some populations almost 20% of differences in gene activity are due to copy-number variants; SNPs account for the rest. People with high-starch diets--such as in Japan--have extra copies of a gene for a starch-digesting protein compared with members of hunting-gathering societies. By scanning the genomes of autistic and healthy children and their parents for copy-number variation, other geneticists have found that newly appeared DNA alterations pose a risk for autism.

New technologies that are slashing the costs of sequencing and genome analyses will make possible the simultaneous genome-wide search for SNPs and other DNA alterations in individuals. Already, the unexpected variation within one individual's published genome has revealed that we have yet to fully comprehend the degree to which our DNA differs from one person to the next. Such structural and genetic variety is truly the spice of our individuality.

Papers and Articles related to Human Genetic Variation

R. Saxena et al., "Genome-Wide Association Analysis Identifies Loci for Type 2 Diabetes and Triglyceride Levels," Science 316, 1331 (2007)

E. Zeggini et al., "Replication of Genome-Wide Association Signals in UK Samples Reveals Risk Loci for Type 2 Diabetes," Science 316, 1336 (2007)

L.J. Scott et al., "A Genome-Wide Association Study of Type 2 Diabetes in Finns Detects Multiple Susceptibility Variants," Science 316, 1341 (2007)

V. Steinthorsdottir et al., "A Variant in CDKAL1 Influences Insulin Response and Risk of Type 2 Diabetes," Nature Genet. 39, 770 (2007)

R. Sladek et al., "A Genome-Wide Association Study Identifies Novel Risk Loci for Type 2 Diabetes," Nature 445, 881 (2007)

J. Sebat et al., "Strong Association of De Novo Copy Number Mutations with Autism," Science 316, 445 (2007)

A.J. de Smith et al., "Array CGH Analysis of Copy Number Variation Identifies 1284 New Genes Variant in Healthy White Males: Implications for Association Studies of Complex Diseases," Hum. Mol. Genet. 16, 2783 (2007)

J.O. Korbel et al., "Paired-End Mapping Reveals Extensive Structural Variation in the Human Genome," Science 318, 420 (2007)

K.K. Wong et al., "A Comprehensive Analysis of Common Copy-Number Variations in the Human Genome," Am. J. Hum. Genet. 80, 91 (2009)

G.H. Perry et al., "Diet and the Evolution of Human Amylase Gene Copy Number Variation," Nature Genet. 39, 1256 (2007)

C.M. Egan et al., "Recurrent DNA Copy Number Variation in the Laboratory Mouse," Nature Genet. 39, 1384 (2007)

The International HapMap Consortium, "A Second Generation Human Haplotype Map of Over 3.1 Million SNPs," Nature 449, 851 (2007)

B.E. Stranger et al., "Population Genomics of Human Gene Expression," Nature Genet. 39, 1217 (2007)

B.E. Stranger et al., "Relative Impact of Nucleotide and Copy Number Variation on Gene Expression Phenotypes," Science 315, 848 (2007)

The Wellcome Trust Case Control Consortium, "Genome-Wide Association Study of 14,000 Cases of Seven Common Diseases and 3,000 Shared Controls," Nature 447, 661 (2007)

J. Fellay et al., "A Whole-Genome Association Study of Major Determinants for Host Control of HIV-1," Science 317, 944 (2007)

C. Lalueza-Fox et al., "A Melanocortin 1 Receptor Allele Suggests Varying Pigmentation Among Neanderthals," Science 318, 1453 (2007)

J. Krause et al., "The Derived FOXP2 Variant of Modern Humans Was Shared with Neandertals," Current Biol. 17, 1908 (2007)

M.N. Weedon et al., "A Common Variant of HMGA2 is Associated with Adult and Childhood Height in the General Population," Nature Genet. 39, 1245 (2007)

P. Sulem et al., "Genetic Determinants of Hair, Eye and Skin Pigmentation in Europeans," Nature Genet. 39, 1443 (2007)

R. McPherson et al., "A Common Allele on Chromosome 9 Associated with Coronary Heart Disease," Science 316, 1488 (2007)

News, Reviews, and Perspectives

J. Couzin and J. Kaiser, "Closing the Net on Common Disease Genes," Science 316, 820 (2007)

J. Novembre et al., "Adaptive Drool in the Gene Pool," Nature Genet. 39, 1188 (2007)

S.A. McCarroll and D.M. Altshuler, "Copy-Number Variation and Association Studies of Human Disease," Nature Genet. 39, s37 (2007)

J. Cohen, "DNA Duplications and Deletions Help Determine Health," Science 317, 1315 (2007)

X. Estivill and L. Armengol, "Copy Number Variants and Common Disorders: Filling the Gaps and Exploring Complexity in Genome-Wide Association Studies," PLoS Genetics 3, e190 (2007)

Interesting Websites

Human Genetic Variation: An NIH Curriculum Supplement
A creative, inquiry-based instruction program, designed to promote active learning and stimulate student interest in medical topics.

International HapMap Project
A multi-country effort to identify and catalog genetic similarities and differences in human beings.

Database of Genotype and Phenotype (dbGaP)
Developed to archive and distribute the results of studies that have investigated the interaction of genotype and phenotype, including genome-wide association studies, medical sequencing, and molecular diagnostic assays.

Genetic Association Information Network (GAIN)
A public-private partnership that aims to understand the genetic factors influencing risk for complex diseases.

ENCODE (Encyclopedia of DNA Elements)
Project launched by the National Human Genome Research Institute (NHGRI) that aims to identify all functional elements in the human genome sequence.

SNPs: A Science Primer
An introduction to single nucleotide polymorphisms, provided by the National Center for Biotechnology Information.

SNPedia
A web site for sharing information about the effects of DNA variations on traits and disease.

The Human Genome: Your Genes, Your Health, Your Future
A comprehensive resource on the human genome, its role in health and medicine, and the broader social impact of unravelling its mysteries; produced by the Wellcome Trust.